Contributed by
PHI University Institute for Radiology Skopje
Biljana Ognenoska, Milkica Pashoska Vasileska, and Vesna Naunova.
History
A 2-year-old child presented with a palpable abdominal mass. Initial ultrasound examination demonstrated a large heterogeneous abdominal tumorous lesion of uncertain origin. Clinical examination revealed associated aniridia, cryptorchidism, and hypospadias. Further imaging evaluation was performed for lesion characterization, determination of organ of origin, and staging. Subsequent CT examination demonstrated a well-defined large tumorous mass with heterogeneous enhancement, possible necrotic or hemorrhagic components arising from the parenchymal bridge of a horseshoe kidney with a “claw sign,” in which the surrounding renal parenchyma appears to wrap partially around the mass.
Images (Click any image to enlarge)
Question
Which syndrome is most strongly associated with these findings?
Your answer
Please log in or register to answer.
Correct answer
Check back 5 hours 27 minutes from now (after 7:00pm) for the answer and further discussion!